| Pulmonary Artery Sling with Situs Solitus Dextroposition of Heart and Left Superior Vena Cava |
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Sung-Ho Cha1, Sung- Yong Jung1, Pill-Jin Shin1, Byong-Soo Cho1, Chang-Il Ahn1, Sun-Wha Lee2 |
1Department of Pediatrics, College of Medicine, Kyunghee University, Seoul, Korea
2Department of Radiology, College of Medicine, Kyunghee University, Seoul, Korea |
| 좌측상대정맥과 심우전위(Dextropositioned Heart)를 동반한 폐동맥슬링(Pulmonary Artery sling) 1례 |
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차성호1, 정성룡1, 신필진1, 조병수1, 안창일1, 이선화2 |
1경희대학교 의과대학교 소아과학교
2경희대학교 의과대학교 방사선과학교실 |
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| Abstract |
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Pulmonary artery sling is a rare congenital cardiovascular anomaly which presents clinical obstructive symptoms and signs of trachea, right main bronchus and esophagus due to left pulmonary artery abnormaly arises from proximal part of right pulmonary artery. Aberrant left pulmonary artery courses to the right above right main bronchus and then turns to the left, and courses to between the anterior of the esophagus and the posterior aspect of trachea. One of important clinical significances of the pulmonary artery sling is associated with intracardiac anomalies, and with tracheal stenosis and bronchomalacia due to press tracheobronchial tree by the aberrant pulmonary artery. It has been thought that embryological malconnection between the pulmonary artery bud from left sixth arch and the pulmonary posterior branchial plexus in the lfet lung bud.
We had experienced 21 months old male infant with left pulmonary artery sling associated with persistent left superior vena cava and dextropostined heart. The heart seems to move to right hemithorax due to hypoplasia or segmental atelectasis of right lung. |
| Key Words:
Pulmonary artery sling, Dextropositioned heart, Left superior vena cava |
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