A Case of Hemimegalencephaly with Intraventricular Hemorrhage and Multifocal Intraparenchymal Hemorrage on Deep White Matter of Periventricular Area |
Jin Sung Ko2, Kook In Park2, Min Soo Park2, Moon Sung Park2, Ran Namgung2, Chul Lee2, Dong Gwang Han2, Choon Sik Yoon1 |
1Department of Diagnostic Radiology, Yonsei University College of Medicine, seoul, Korea 2Department of Pediatrics, Yonsei University College of Medicine, seoul, Korea |
뇌실내 출혈 및 다발성 뇌실주위 백질 출혈이 동반된 편측성 대두개 1례 |
고진성2, 박국인2, 박민수2, 박문성2, 남궁란2, 이철2, 한동관2, 윤춘식1 |
1연세대학교 의과대학 진단방사선과학교실 2연세대학교 의과대학 소아과 |
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Abstract |
Hemimegalencephaly is a rare congenital anomaly characterized by a intractable seizure an infantile death. This disease is a migrational disorder with enlargement of unilateral hemisphere, abnormal gyration of the cortex, the presence of large and atypical neuron, hetero trophic neuron at subcortical area and proliferation of astrocyte ect.
We observed a neonate with neonatal seizure, and the radiological evaluation revealed abnormal enlargement of right hemisphere, intraventricular hemorrhage of both ventricle and multifocal intraparenchymal hemorrhage on deep white matter of periventricular area on both sides. We used the phenobarbital for treatment of seizure. After phenobarbital treatment. The seizure was controlled.
A review of literature was also presented briefly |
Key Words:
Hemimegalencephaly, Neonate |
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