A Case of Renal Hypoplasia with Renovascular Hypertension |
Sang Doo Lee1, Jae Hee Park1, Jae Beom Lee1, Yun Duk Yoo1, Byoung Hwa Lee1, Mi Sun Lee2 |
1Department of Pediatrics, Sun General Hospital, Daejeon, Korea 2Department of of Pathology, Sun General Hospital, Daejeon, Korea |
신형성부전에 의한 신성 고혈압 1례 |
이상두1, 박재희1, 이재범1, 유연덕1, 이병화1, 이미선2 |
1대전 선병원 소아과학교실 2대전 선병원 해부병리과 |
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Abstract |
Renal hypoplasia is a condition in which the kidneys are small because of developmental parenchymal deficit. Essential to this definition is the notion of normally developed and differentiated individual nephrons and ducts, without coexisting dysplasia. Affected renal artery and intrarenal blood vessel branches are relatively hypoplastic and commonly sclerotic. Stenosis of main arteries or its branches are apt to cause hypertension. The pathogenesis of hypoplastic kidneys may involve a diminished number of nephrons and diminished nephrotic size.
We experienced a 4-year-old boy with 180/130mmHg of blood pressure, and confirmed renovascular hypertension due to a typical unilateral renal hypoplasia. Nephrectomy was done and the blood pressure returned to normal. Abdominal ultrasonogram, CT, aortic angiography, and pathologic findings are presented with a brief review |
Key Words:
Renal hypoplasia, Renovascular hypertension, Nephrectomy |
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