| Bone Age Determination and Hand Radiographic Findings in Children With Russell-Silver Syndrome. |
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Hun Kyu Lim, Sei Won Yang, Hyung Ro Moon |
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Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea |
| Russell-Silver 증후군 환아들의 골연령 및 수장골의
방사선학적 소견 |
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임헌규, 양세원, 문형로 |
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서울대학교 의과대학 소아과학교실 |
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Received: 26 November 1988 • Accepted: 13 December 1988 |
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| Abstract |
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Russell.Silver syndrome is a disease of unknown etiology characterized by prenatal onset dwarfism
irrespective of full term gestation, growth retardation, body asymmetry, craniofacial dysproportion
with a triangular face, short and incurved little finger, etc.
Forty.two children were diagnosed as Russell.Silver syndrome by Silver’s criteria at SNU Children'
s Hospital from Apr. 1981 till Aug. 1988, and we reviewed clinical data and hand radiographs of the
patients
Mean birth weight was 2,300 g with term gestation in 38 (91 %). Mean body weight and height were
below the 3rd percentile of normal children but growth velocity of the patients was similar to those
of the 3rd percentile of normal children (p< 0.05).
Bone age was delayed in 39 (95%) of 41 children and normal in 2 (5%), and it could be a good
indicator in predicting the body weight and height of children with Russell.Silver syndrome.
In hand radiographs, hypoplasia of little finger was noted in 93% of 41 children, ivory epiphysis in
39%, and pseudoepiphysis in 34%. |
| Key Words:
Russell.Silver Syndrome, Growth Velocity, Bone Age, Hypoplasia of little Finger, Ivory
Epiphysis, Pseudoepiphysis |
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