A Case Report of Systemic Mastocytosis. |
Kwang Tae Chung1, Ja hoon Koo1, Sae Kwang Moon2 |
1Department of pediatrics, Kyung Pook National University, School of Medicine, Taegu, Korea. 2Deprtment of Pathology, Fatima hospital, Taegu, Korea. |
肥肝細胞症(色素性蕁麻疹)의 一例 |
鄭光兌1, 具慈薰1, 文世光2 |
1慶北醫犬 小兒科學敎室 2大邱파티마病院 臨床病理科 |
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Abstract |
A case of systemic mastocytosis in a 6 year old boy was presented. Skin lesions started to appear and spred several days after birth along with severe itching sensation, and intermitent abdominal pain & constipation developed at the age of 5. On physical examination, he was found to be underdeveloped (Height less than 3rd percentile) with normal vital signs. Liver was felt 1 1/2 fb below costal margin, spleen 2 fb. There were many brown to dark brown-colored irregular shaped maculopapulourticarial skin lesions, scattered all over the body, along with multiple thickened areas, and positive Darier's sign was noted. On upper GI series, many honey-combed filling defect were found throughout small intestine. Skin biopsy confirmed the diagnossis : showing multiple scattered infilteration of mast cells. |
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