Clinical Review of Progressive Muscular Dystrophy |
Shin Hyung Chang, Ze Bo Cho, Ji Sub Oh, Dong Hyuk Kim, Dong Hak Shin |
Department of Pediatrics, Presbyterian Hospital Taegu, Korea |
進行性 筋奏縮症의 臨床的 觀察 |
裝信炯, 趙在寶, 吳智燮, 琴東盧, 申東鶴 |
大邱東山基督病院小兒科 |
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Abstract |
The authors has observed 19 patients of progressive muscular dystrophy who were admitted to the
Pediatric department and Orthopedic department and diagnosed by clinical symptoms, urine findings
and muscle biopsy during the period from Mar. 1960 to April 1971.
The results are as follows:
1) The most common form was Dechenne type (84.1%) and
2) All cases were male
3) In Duchenne type, the case of onset under 5 years old was 9 cases (56.25%)
4) Urinary creatine excretion was decreased, while urinary creatine value was elevated and so
urinary creatine-creatinine ratio was decreased.
5) In Duchenne type, mental retardation was noted in 4 cases (25%).
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