| A Case of Rotor Syndrome |
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Jin Nyoung Park, In Joon Seol |
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Department of Pediatrics, College of Medicine, Hanyang University, Seoul, Korea |
| Rotor 증후군 1례 |
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박진녕, 설인준 |
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한양대학교 의과대학 소아과학교실 |
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| Abstract |
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We experienced a case of Rotor syndrome in an 8 year 6 month old boy who presented with icteric sclera and icteric skin on whole body. His clinical and laboratory characteristics were as follows;
1) Jaundice appeared from several months ago before admission without any clinical disturbance.
2) Direct bilirubin was more increased than indirect bilirubin.
3) Plasma indocyanine green (ICG) kinetics test revealed hepatic excretory defect in this patient that after intravenous injection of a standard dose of ICG (0.5 mg/kg), its initial plasma disappearance is decreased, resulting in markedly increased retention of the dye 45 to 50 minutes after administration.
4) Oral cholangiography, ultrasonogram, and computed tomogram of abdomen were normal.
5) Liver biopsy specimen showed no dark brown pigmentations in the hepatic cells and any other pathologic abnormalities.
6) Nearly similar clinical and laboratory findings were observed 26 months later. |
| Key Words:
Rotor Syndrome |
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