| A Case of Pulmonary Blastoma |
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Yun Jeong Chang1, Jeong Hee Kim1, Sun Ki Kim1, Byong Kwan Son1, Joon Mi Kim2, Young Chae Chu2 |
1Department of Pediatrics, Inha University Medical College, Sung Nam, Korea
2Department of Anatomical Pathology, Inha University Medical College, Sung Nam, Korea |
| 폐아세포종 1례 |
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장윤정1, 김정희1, 김순기1, 손병관1, 김준미2, 주영채2 |
1인하대학교 의과대학 소아과학교실
2인하대학교 의과대학 해부병리과학교실 |
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| Abstract |
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Pulmonary blastoma is a rare type of malignant lung tumor comprised of epithelial and mesenchymal elements reminiscent of fetal lung. Mesenchymal element may show various patterns of differentiation toward mature tissue, such as cartilage, smooth muscle, and bone. Rhabdomyoblastic differentiation in pulmonary blastoma is quite rare. Our case of pulmonary blastoma with rhabdomyoblastic differentiation documented by electron microscopy and immunohistochemistry.
Usually it has been treated with surgery, but both chemotherapy and radiotherapy have been used against the metastatic disease, and as the adjuvant setting.
A 28/12-year-old girl is described who was presented with pulmonary blastoma. She underwent surgical excision of the tumor, followed by the T2protocol, a 8 cycles of combination chemotherapy consisting of actinomycin-D, adriamycin, vincristine and cyclophosphamide with the radiation therapy to the left chest cage(180 cGy¡¿11times). The patient has been off therapy without any evidence of relapse for 24 months. We report a case of pulmonary blastoma with brief review of related literatures. |
| Key Words:
Pulmonary blastoma, Rhabdomyoblastic differentiation, Surgical excision, Combination chemotherapy, Radiation therapy |
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