A Case of Nonfamilial Generalized Gastrointestinal Juvenile Polyposis with Pancytopenia |
Jong Ook Kim1, Heung Pyo Kong1, Kang Seo Park1, Wan Seob Kim1, Chun Hee Lee2 |
1Department of Pediatrics, Presbyterian Medical Center, Chonju, Korea 2Department of Clinical Pathology Presbyterian Medical Center, Chonju, Korea |
범혈구 감소증이 동반된 범 위장관 연소성 용종증 1례 |
김종욱1, 공흥표1, 박강서1, 김완섭1, 이춘희2 |
1전주예수병원 소아과 2전주예수병원 임상병리과 |
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Abstract |
In contrast to the child with a solitary juvenile polyp, generalized gastrointestinal juvenile polyposis have a much different clinical course. In generalized juvenile polyposis blood loss can be considerable and iron-deficiency anemia is a common observation. Although it is usually regarded as a benign condition, juvenile polyposis may predispose to cancer of the gastrointestinal tract.
We experienced a case of nonfamilial generalized gastrointestinal juvenile polyposis with pancytopenia in a 15 year-old male patient who had hospitalized because of intermittent rectal bleeding with anemia for three years. Histological examination of polyps from affected patient revealed a spectrum of change from juvenile polyps, to juvenile polyps with adenomatous changes. Subtotal colectomy, rectal mucosectomy, and endorectal pull-through procedure were successfully performed. No complication has occured since the discharge. A brief review of related literatures is also presented. |
Key Words:
Juvenile polyposis, GI tract, Pancytopenia |
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