| A Case of Hypothalamic Hamartoma with Gelastic Seizure Only |
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Se Wook Oh, Je Ho Cho, Sang Woo Kim |
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Department of Pediatrics, Seoul Paik Hospital, College of Medicine, Inje University, Seoul, Korea |
| 시상하부 과오종에 동반된 GelasticEpilepsy 1례 |
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오세욱, 조재호, 김상우 |
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인제대학교 의과대학 서울백병원 소아과 |
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| Abstract |
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Hypothalamic hamartoma is a congenital anomaly presenting precocious puberty, gelastic seizure and mental retardation. Other possible accompanying anomalies are cleft palate, tetralogy of Fallot, skeletal malformation and anal malformation. But the patient describing here manifested gelastic seizure only with isosignal mass of 1.5cm in diameter situated just behind optic chiasm in T1WI and T2WI of MRI. His EEG showed multifocal spike and sharp waves at left frontal and central area with asymmetric sleep spindles. The seizure has been refractory to conventional antiepileptic drugs. He is now on Lamotrigine, a newly developed antiepileptic drug available. |
| Key Words:
Hypothalamic hamartoma, Gelastic seizure |
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