A Case of Neurofibromatosis with Multiple Neurofibromas on Mesentery |
Pil Geung Hwang, Sun Young Park, Tae Gyu Whang, Soon Yong Lee |
Department of Pediatrics, College of Medicine, Inje University Pusan Paik Hospital, Pusan, Korea |
장간막의 다발성 신경섬유종을 동반한 신경섬유종증 1례 |
황필경, 박선영, 황태규, 이순용 |
인제대학교 의과대학 소아과학교실, 부산백병원 |
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Abstract |
Neurofibromatos is originally described by von-Recklinhausen in 1882, is often depicted as a chronic progressive hereditary disease characterized by pigmentation of the skin, cutaneus lesions, and numerous tumors developing in association with elements of both the central and peripheral nervous tissue. Mesenteric involvements in neurofibromatosis are very rare in childrens.
We experienced a case of neurofibromatosis with multiple neurofibromas on mesentery
in 6 years old male who presented with abdominal pain. The diagnosis was confirmed
by clinical manifestations, abdominal CT, and histopathologic findings.
Brief review of literatures was made. |
Key Words:
Neurofibromatosis, Neurofibromas, Mesentery |
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