| A Case of Congenital Megacalyces |
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Kyeong Mee Lee, Ran Joo Kim, Dae-Yeol Lee |
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Department of Pediatrics, Chonbuk National University Medical School, Chonju, Chonbuk, Korea |
| 선천성 거대신배 (Congenital megacalyces) 1례 |
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이경미, 김란주, 이대열 |
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전북대학교 의과대학 소아과학교실 |
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| Abstract |
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Congenital megacalyces is a congenital renal disease characterized by hypoplasia of the medulla
and a non-obstructive dilatation of the calyces. More than 100 cases have been reported in the
literature after first described by Puigvert in 1963, but it has been reported only three cases(two
cases of adults and one case of child) in the literatures in Korea.
The etiology of the congenital megacalyces is unknown. Renal pelvis and ureter are mostly normal
in size and there is no urinary obstruction or reflux. Renal medulla of congenital megacalyces is
thinner than that of normal kidney but renal cortex retains its normal thickness and function. This
is features that help to distinguish megacalyces from obstructive atropy. The calyces are polygonal
in shape and the majority of kidney with megacalyces have increased number of calyces. Since
congenital megacalyces is a non-progressive lesion, it is important to recognize the clinical entity
and avoid unnecessary surgery.
We report one case of congenital megacalyces without urinary obstruction or reflux with a brief
review of related literatures. |
| Key Words:
Megacalyces, Urinary obstruction, Reflux |
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