| A Case of Omphalocele-Exstrophy-Imperforate Anus-Spina Bifida(OEIS syndrome) |
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Hyeon Jong Yang, Lae Kyung Park, Han Jin Kim, Hye Kyung Lee, Young Chang Kim |
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Department of Pediatrics, College of Medicine, Soonchunhyang University, Chunan, Korea |
| Omphalocele-Exstrophy-Imperforate Anus-Spinal Defects(OEIS) 증후군 1례 |
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양현종, 박래경, 김한진, 이혜경, 김영창 |
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순천향대학교 의과대학 소아과학교실 |
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| Abstract |
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Omphalocele-exstrophy-imperforate anus-spinal defects(OEIS Syndrome) is a single defect in early mesoderm, and its incidence is about one in 250,000. If was first described by Littre in 1709. The characteristics of this disorder is omphalocele, extrpohy of bladder, imperforate anus and spina bifida. There have been reports of longtime survival made possible by several operations, but for most cases normal life is impossible due to the deformities. We report a case of OEIS complex who had omphalocele, exstrophy of bladder, imperforate anus and spina bifida from birth. |
| Key Words:
OEIS syndrome |
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