A Case of Distal Renal Tubular Acidosis Associated with Medullary Sponge Kidney |
Sung Jun Jang1, Jo Yun Jung1, Jun Sik Kim1, Heung Sik Kim1, Hee Jung Lee2 |
1Department of Pediatrics, School of Medicine, Keimyung University, Daegu, Korea 2Department of Diagnostic Radiology, Keimyung University, Daegu, Korea |
Medullary Sponge Kidney에 동반된 원위형 신세뇨관 산혈증 1례 |
장성준1, 조윤정1, 김준식1, 김흥식1, 이희정2 |
1계명대학교 의과대학 소아과학교실 2계명대학교 의과대학 진단방사선학교실 |
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Abstract |
Renal tubular acidosis is a clinical state of systemic hyperchloremic acidosis resulting from impaired urine acidification. Medullary sponge kidney is a renal parenchymal malformation characterized by cystic dilatation of the collecting ducts. Although medullary sponge kidney is a congenital disease, it is rarely identified in childhood and is usually discovered in adulthood. Medullary sponge kidney patients may have defects in urinary acidification and concentration mechanism. We experienced a case of distal renal tubular acidosis associated with medullary sponge kidney. So, we report a case of distal renal tubular acidosis associated with medullary sponge kidney with a brief review of the related literature. |
Key Words:
Medullary sponge kidney, Distal renal tubular acidosis |
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