A Case of Congenital Nasal Pyriform Aperture Stenosis |
Hyoung Sik Oh1, Sang Hee Kim1, Gil Hyun Kim1, Hak Soo Lee1, Il Hwan Jang2, Ji Hae Kim3 |
1Department of Pediatrics, Gachon Medical School, Incheon, Korea 2Department of Otolaryngology, Gachon Medical School, Incheon, Korea 3Department of Diagnostic Radiology, Gachon Medical School, Incheon, Korea |
선천성 비이상구 협착증 1례 |
오형식1, 김상희1, 김길현1, 이학수1, 장일환2, 김지혜3 |
1가천의과대학 소아과학교실 2가천의과대학 이비인후과학교실 3가천의과대학 방사선과학교실 |
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Abstract |
The cause of congenital nasal pyriform aperture stenosis is unclear. The development of the facial skeleton occurs between the fifth and the eighth week of gestation. It is at this stage that the stenosis occurs due to overgrowth of the ossification of the maxilla. Infants are obligate nasal breathers. Incomplete and milder forms of nasal airway obstruction may be present with mild respiratory distress, cyanosis, respiratory failure, asphyxia and eventual death. The diagnosis is done by CT, which demonstrates marked narrowing of the nasal inlet. Mild stenosis can be managed conservatively with humidification and topical decongestants but if conservative treatment fails, surgical intervention is candidate. We report a case of congenital nasal pyriform aperture stenosis. The patient, a 2-day old male neonate, had cyanosis during feeding and noisy breathing relieved by crying. His symptoms and signs were improved with surgical intervention without development disturbances. |
Key Words:
Congenital nasal pyriform aperture stenosis, Respiratory distress, Cyanosis |
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