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A Case of Satoyoshi Syndrome Presented with Progressive Muscular Spasm and Alopecia

Journal of the Korean Pediatric Society 2002;45(9):1165-1169.
Published online September 15, 2002.
A Case of Satoyoshi Syndrome Presented with Progressive Muscular Spasm and Alopecia
Kyung Ran Son1, Jin Hwa Kook1, Byung Ju Kim1, Sung Jin Kim2, Jae Sook Ma1
1Department of Pediatrics, Chonnam National University, Medical School, Gwangju, Korea
2Department of Dermatology, Chonnam National University, Medical School, Gwangju, Korea
근 경련과 전신성 탈모증을 보인 Satoyoshi 증후군 1례
손경란1, 국진화1, 김병주1, 김성진2, 마재숙1
1전남대학교 의과대학 소아과학교실
2전남대학교 의과대학 피부과학교실
Correspondence: 
Byung Ju Kim, Email: kimbj@chonnam.ac.kr
Abstract
Satoyoshi syndrome(generalized Komuragaeri disease) is a rare disorder of unknown cause, characterized by progressive, painful, intermittent muscle spasms and alopecia. Endocrinopathy with amenorrhea, secondary skeletal abnormalities, and diarrhea or unusual malabsorption are frequently seen. It seems that autoimmunity may play a role in its pathogenesis. We report a 13-year-old girl with characteristic manifestations of the syndrome. She was treated with intravenous gammaglobulin and Prednisolone. Painful muscle cramps were gradually improved, but the scalp condition did not change. Satoyoshi syndrome should be considered in children with unexplained muscle spasms and alopecia.
Key Words: Satoyoshi syndrome, Muscle spasm, Alopecia


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