| Familial Sick Sinus Syndrome |
|
In-Hye Nam, Sung-Hee Cheon, Hong-Ryang Kil |
|
Department of Pediatrics, College of Medicine, Chungnam National University, Daejeon, Korea |
| 가족성 동기능 장애 증후군 1례 |
|
남인혜, 천성희, 길홍량 |
|
충남대학교 의과대학 소아과학교실 |
Correspondence:
Hong-Ryang Kil, Email: namine726@hanmail.net
|
|
|
|
|
| Abstract |
|
Sick sinus syndrome(SSS) constitutes a spectrum of cardiac arrhythmia, including sinus bradycardia, sinus pause-arrest, sinoatrial block, slow escape rhythm, bradyarrhythmia and tachyarrhythmia. SSS is relatively uncommon in children but its exact incidence is unknown because diagnostic criteria are not uniform and most children with SSS, in general are asymptomatic. SSS may be primary(organic sinus node disease) or secondary(cardiac surgery comprises much of SSS in children and adolescents), but it can hardly be caused by familial relations as well. We reports an occurrence of familial sick sinus syndrome. Mother was diagnosed as SSS, which was presented by symptoms of dizziness and treated by permanent pacemaker(DDD). Also, two daughters revealed SSS with non- compacted cardiomyopathy on neonatal screening and fetal echocardiography respectively. We concluded that familial SSS may occur, so familial screening should be suggested. |
| Key Words:
Sick sinus syndrome, Cardiomyopathy |
|
PDF Links
Download Citation
