A Case of Systemic Sclerosis in a Child |
Ji Yeon Chang1, Ja Kyoung Kim1, Jeong Hee Kim1, Dae Hyun Lim1, Byong Kwan Son1, Jung Soo Song2 |
1Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea 2Department of Internal Medicine, College of Medicine, Inha University, Incheon, Korea |
소아에 발생된 전신성 경화증 1례 |
장지연1, 김자경1, 김정희1, 임대현1, 손병관1, 송정수2 |
1인하대학교 의과대학 소아과학교실 2인하대학교 의과대학 내과학교실 |
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Abstract |
Systemic sclerosis is a connective tissue disease involving primarily the skin and subcutaneous tissue but may involve other organ systems such as the lungs, gastrointestinal tract, and heart. Systemic sclerosis is a rare childhood disease. The age of onset for patients with systemic sclerosis has its peak between 30 and 50 years of age. Only 1 to 2% of all patients with systemic sclerosis have disease onset before the age of 10 years of age. We report a case of systemic sclerosis in a 7- year-old female who showed Raynaud's phenomenon as an initial manifestation. |
Key Words:
Raynaud's phenomenon, Systemic sclerosis |
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