Surgical Correction of Congenital Heart Disease In 18 Trisomy |
Jinyoung Song1, Yun Hee Moon2, Ki Young Jang1, Jae Young Lee1, Soo Jin Kim1, Woo Seup Shim1, Woong Han Kim3 |
1Department of Pediatrics, Sejong General Hospital, Buncheon, Korea 2Department of Pediatrics, College of Medicine, Kyunghee University, Seoul, Korea 3Department of Thoracic Surgery, Seoul National University College of Medicine, Seoul, Korea |
에드워드 증후군에서 선천성 심질환을 수술로 교정한 1례 |
송진영1, 문윤희2, 장기영1, 이재영1, 김수진1, 심우섭1, 김웅한3 |
1부천세종병원 소아과 2경희대학교 의과대학 소아과학교실 3서울대학교 의과대학 소아과학교실 |
Correspondence:
Jinyoung Song, Email: amyjys@hanmail.net |
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Abstract |
18 trisomy(Edwards syndrome) is a fatal disease with a congenital heart anomaly. Patients usually receive less aggressive care because caregivers expect them to die very young. Although they have a very poor prognosis due to severe multi-organ dysfunction, symptomatic simple cardiac anomaly with left to right shunt can be repaired. We experienced a case of 18 trisomy with ventricular septal defect and patent ductus arteriosus. He showed prolonged dyspnea and tachypnea after the ligation of patent ductus arteriosus in a previous hospital. In our hospital, the ventricular septal defect was closed because his parents insisted on aggressive treatment. After surgery, the symptoms were relieved and he was discharged in a condition satisfactory to his parents and the medical team. |
Key Words:
Trisomy, Heart defect, Congenital |
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