Melanotic Neuroectodermal Tumor of Infancy in the Epididymis : A Case Report |
Sang Bae Lee1, Seong Hun Lee1, Min Hyuk Ryu1, Ji Seoung Park2, Joo Heoun Yang2, Sun Young Kim1, Dong Jean Lee1 |
1Department of Pediatrics, Urology* and Pathology†, Dong Kang General Hospital, Ulsan, Korea 2Department of Pediatrics, Urology* and Pathology†, Dong Kang General Hospital, Ulsan, Korea |
부고환에 발생한 영아기 흑색 신경외배엽성 종양 1례 |
이상배1, 이성훈1, 류민혁1, 박지성2, 양주현2, 김선영1, 이동진1 |
1울산 동강병원 소아과 2울산 동강병원 비뇨기과 |
Correspondence:
Dong Jean Lee, Email: djleekr@hanmail.net |
|
|
Abstract |
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare neoplasm known by a variety of names including melanotic progonoma and retinal anlage tumor, and currently thought to be neural crest derivation. The vast majority develop within the first year of life. The behavior is generally benign, but recurrent and metastatic cases have been documented. It arises in the head and neck in over 90%, mainly in the maxilla, but is extremely rare in the epididymis. We report a case of MNTI together with a review of literature, which occurred in the right epididymis of a 6-month-old boy who presented with a painless, slowly growing, scrotal mass and was treated with radical orchiectomy. |
Key Words:
Melanotic neuroectodermal tumor of infancy , Epididymis |
|