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A Case of Choledochal Cyst Complicated by Liver Cirrhosis on Pathology in a 20-Month-Old-Girl

Korean Journal of Pediatrics 2005;48(1):104-107.
Published online January 15, 2005.
A Case of Choledochal Cyst Complicated by Liver Cirrhosis on Pathology in a 20-Month-Old-Girl
Sun Hwan Bae1, Sung Yun Choi2, Tae Seok Lee3, Ho Jeong Lee4
1Department of Pediatrics, School of Medicine, Konkuk University, Seoul, Korea
2Department of Pediatrics, School of Medicine, Eul-Ji University, Seoul, Korea
3Department of General Surgery, School of Medicine, Eul-Ji University, Seoul, Korea
4Department of General Surgery, School of Medicine, Eul-Ji University, Seoul, Korea
수술 후 임상증상이 호전된 간경화를 합병한 2세 여아에서의 총수담관낭 1례
배선환1, 최성윤2, 이태석3, 이호정4
1건국대학교 의과대학 소아과학교실
2을지의과대학교 소아과학교실
3을지의과대학교 일반외과학교실
4을지의과대학교 해부병리학교실
Correspondence: 
Sun Hwan Bae, Email: baedori@hanafos.com
Abstract
Choledochal cyst is considered to be congenital anomalies of the biliary tract, characterized by varying degrees of cystic dilatation at various segments of the biliary tract. A 20-month-old girl was admitted to Eul-Ji general hospital because of abdominal distension. Physical examination revealed marked splenomegaly and hepatomegaly with nodular surface and hard consistency. Laboratory examination showed elevated transaminase level, alkaline phosphatase level and gamma glutamyltranspeptidase level without evidence of cholestasis. Diagnostic imaging study revealed choledochal cyst with Todani classification type 1. Cholecystectomy and Roux-en-Y choledochojejunostomy was performed, and wedge liver biopsy showed diffuse periportal fibrosis with cirrhotic change and ductular proliferation in the portal area. After operation, hepatosplenomegaly and abnormal laboratory examinations improved rapidly, and in 9 months, the liver and spleen became not palpable. We experienced a case of choledochal cyst complicated by liver cirrhosis on pathology in a 20 month-old girl, and removal of choledochal cyst improved clinical manifestations rapidly.
Key Words: Choledochal cyst, Liver cirrhosis, Child


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