| A Case of Infantile Hemangioendothelioma of the Liver Treated with Hepatic Embolization and Lobectomy |
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Jae Seon Kim1, Soo Kyung Moon1, Hye Sun Yoon1, Tae Seok Lee2 |
1Department of Pediatrics, School of Medicine, Eulji University, Seoul, Korea
2Department of Pediatric Surgery, School of Medicine, Eulji University, Seoul, Korea |
| 간동맥 색전술과 간엽 절제술로 치료한 영아 간내 혈관내피종 1례 |
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김재선1, 문수경1, 윤혜선1, 이태석2 |
1을지의과대학교 노원을지병원 소아과
2을지의과대학교 노원을지병원 소아외과 |
Correspondence:
Hye Sun Yoon, Email: yhs3211@eulji.or.kr
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| Abstract |
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Infantile hemangioendothelioma(IHE) of the liver is the most common vascular tumor in infants before the age of 6 months. It is a histologically benign tumor with potentially life-threatening complications. The clinical manifestations are variable, ranging from asymptomatic forms to intractable high-output heart failure. In addition, abdominal mass, intraperitoneal hemorrhage due to rupture of mass, respiratory distress, hematologic abnormalities and jaundice can occur. Diagnostic work-up is through doppler ultrasound sonography, computed tomography scan, magnetic resonance imaging and angiography. Treatment consists of medical treatment, interventional therapy, surgical resection and liver transplantation. We experienced symptomatic IHE in a premature neonate who presented with high output heart failure and respiratory distress. Initial medical treatment and steroid therapy failed to improve his condition. Coil embolization of left hepatic artery resulted in improvement of respiratory symptoms. However, a left lobectomy was performed because the mass size was not decreased with development of collateral vessels. The infant was well, after a successful discharge from the hospital. |
| Key Words:
Infantile hemangioendothelioma , Coil embolization , Lobectomy , Liver |
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