| Intervention with Balloon Valvuloplasty followed by Patent Ductus Arteriosus Stent in a Patient with Pulmonary Atresia with Intact Ventricular Septum |
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Han Hyuk Lim1, Young Deuk Kim1, Jae Hwan Lee1, Mea Young Chang2, Hong Ryang Kil1 |
1Department of Pediatrics, College of Medicine, Chungnam National University, Daejeon, Korea
2Department of Internal Medicine, College of Medicine, Chungnam National University, Daejeon, Korea |
| 풍선판막성형술과 동맥관 스텐트를 이용하여 치료한 심실중격결손을 동반하지 않은 폐동맥 폐쇄 1례 |
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임한혁1, 김영득1, 장미영1, 이재환2, 길홍량1 |
1충남대학교 의과대학 소아과학교실
2충남대학교 의과대학 내과학교실 |
Correspondence:
Hong Ryang Kil, Email: gilhong@cnu.ac.kr
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| Abstract |
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Pulmonary atresia with intact ventricular septum (PAIVS) is rare, less than 1% of congenital heart disease. It needs a therapeutic approach according to its individual morphologic feature. Surgical treatment of valvotomy and modified Blalock-Taussig shunt or non-surgical interventional catheter balloon valvuloplasty can be used for mild to moderate hypoplasia of right ventricle. Fontan operation can be considered for less optimum morphological substrate of two ventricular repair. A 3- day-old male neonate was admitted with cyanosis and cardiac murmur. On echocardiogram, he had membranous pulmonary atresia with intact ventricular septum, normal sized tripartite right ventricle, large atrial septal defect with right-to-left shunt, small sized patent ductus arteriosus, and moderate tricuspid regurgitation. He was treated with intravenous continuous infusion of prostaglandin E1 (PGE1) at once. On the third day of hospitalization, Balloon valvuloplasty was performed. After insertion of patent ductus arteriosus stent on the tenth day, PGE1 infusion was discontinued. On the fifteenth day, he was discharged. Now, he is 9 months old and has nearly normal cardiac structure and function with 97% of percutaneous oxygen saturation. |
| Key Words:
Pulmonary Atresia , Balloon Valvuloplasty , Stent |
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