| A case of hepatopulmonary syndrome in a child with fatty liver disease secondary to hypopituitarism after craniopharyngioma resection |
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Sun Ju Im, Hyun Seok Park, Hyoung Doo Lee, Jae Hong Park, Hee Ju Park |
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Departments of Pediatrics, College of Medicine, Pusan National University, Busan, Korea |
| 지방간을 가진 소아에서 두개인두종 절제술 후의 뇌하수체기능저하증으로 인해 급격하게 진행된 간-폐 증후군 1예 |
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임선주, 박현석, 이형두, 박재홍, 박희주 |
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부산대학교 의과대학 소아과학교실 |
Correspondence:
Hee Ju Park, Email: phj7294@hanmail.net
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| Abstract |
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Hepatopulmonary syndrome is a triad that includes: hepatic dysfunction, intrapulmonary vascular dilatation and abnormal arterial oxygenation. The incidence of intrapulmonary vascular dilatations, in adults with end-stage liver disease, has been reported to be 13% to 47%, however the incidence in children is unclear and the cases in Korean children have never been reported. The hepatopulmonary syndrome may occur as a result of chronic liver disease following nonalcoholic steatohepatitis in children with hypothalamic or pituitary dysfunction. We report a case of hepatopulmonary syndrome in a 13-year- old child who had rapidly progressive liver dysfunction secondary to panhypopituitarism after craniopharyngioma resection. Careful monitoring and treatment of endocrine abnormalities and metabolic status, as well as liver function, are required in all children undergoing pituitary tumor resection. |
| Key Words:
Hepatopulmonary syndrome, Fatty liver disease, Hypopituitarism, Craniopharyngioma |
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