Primary leiomyosarcoma of the chest wall in a child :
a case report |
Jae Hyuk Choi, David Chanwook Chung, Mee Jeong Lee |
Department of Pediatrics, Dankook University College of Medicine, Cheonan, Chungnam, Korea |
소아의 흉벽에서 진단된 평활근육종 1례 |
최재혁, 정찬욱, 이미정 |
단국대학교 의과대학 소아청소년과학교실 |
Correspondence:
Mee Jeong Lee, Email: LMJPED@dankook.ac.kr |
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Abstract |
Leiomyosarcoma is an uncommon soft tissue sarcoma of mesenchymal cell origin, which shows smooth muscle differentiation. Leiomyosarcoma is seldom found in the pediatric population, and accounts for fewer than 2% of all soft tissue sarcomas. Leiomyosarcoma of the chest wall is extremely rare in children. We report here a case of an 8-year-old boy with a primary leiomyosarcoma that was incidentally found as a rib mass. The patient underwent a complete resection for a suspected osteochondroma diagnosed by a three-dimensional chest computed tomography examination. Pathological findings of the mass revealed intersecting fascicles of spindle cells showing cigar-shaped nuclei, inconspicuous nuclear pleomorphism and occasional mitotic figures in the background of a suspected osteochondroma of the rib. This report documents the first description of a leiomyosarcoma possibly arising in an osteochondroma of the rib in a child. |
Key Words:
Leiomyosarcoma, Chest wall, Rib, Osteochondroma, Child |
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