A case of idiopathic pulmonary hemosiderosis with seasonal recurrence |
Ga Young Kwak, Na Young Lee, Moon Hee Lee, Soo Young Lee, Seung Yun Chung, Jin Han Kang, Dae Chul Jeong |
Department of Pediatrics, College of Medicine, The Catholic University of Korea |
계절성으로 재발한 특발성 폐 혈철 침착증 1예 |
곽가영, 이나영, 이문희, 이수영, 정승연, 강진한, 정대철 |
가톨릭대학교 의과대학 소아과학교실 |
Correspondence:
Dae Chul Jeong, Email: dcjeong@catholic.ac.kr |
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Abstract |
Idiopathic pulmonary hemosiderosis (IPH) is a rare disease affecting mostly children. This disorder is characterized by recurrent episodes of hemoptysis, bilateral diffuse pulmonary infiltrates, and iron-deficiency anemia. An acute fulminant alveolar hemorrhage can be fatal due to respiratory failure, while chronic hemorrhage leads to hemosiderin-laden macrophages and pulmonary fibrosis. Genetic, autoimmune, allergic, environmental, and metabolic mechanisms of pathogenesis have been suggested, but the etiology of IPH remains unknown. We report on a 9-year-old girl with idiopathic pulmonary hemosiderosis who showed seasonal recurrences without cause. |
Key Words:
Idiopathic pulmonary hemosiderosis, Seasonal recurrence |
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