A case of myelofibrosis with juvenile xanthogranuloma. |
Jong Chan Kim1, Hae Yong Lee1, Hwang Min Kim1, Baek Keun Lim1, Jong Soo Kim1, Young Hyuk Lee2 |
1Department of Pediatrics, Yonsei University, Wonju College of Medicine, Wonju, Korea. 2Department of Pediatrics, Min Joong HospitaI,Konkuk University, College of Medicine |
연소성 황색육아종과 동반된 골수섬유증 1례 |
김종찬1, 이해용1, 김황민1, 임백근1, 김종수1, 이영혁2 |
1연세대학교 원주의대 소아과학교실 2건국대학교부속 민중병원 소아과 |
Received: 20 November 1990 • Accepted: 26 February 1991 |
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Abstract |
Myelofibrrosis is characterized by anemia, leukoerythroblastosis, extramedullary hematopoiesis,
hepatosplenomegaly, osteosclerosis and fibrosis of bone marrow. Idiopathc myelofibrosis is usually a
disease of the adult and is rare in the pediatric age group. Juvenile xanthogranuloma is characterized
by multiple papules on forehead and scalp. Lipid laden histiocytes and Touton giant cell are found in
skin biopsy. We experienced a case of myelofibrosis with juvenile xanthogranuloma. So, we presented
the case and brief review of literatures. |
Key Words:
Mylofibrosis, Juvenile xanthogranuloma |
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