Two Cases of Cerebral Gigantism (Sotos Syndrome). |
Hee Jeung Ahn, Young Tae Kim, In Hoon Seol, Jeh Hoon Shin |
Department of Pediatrics, Hanyang University College of Medicine, Seoul, Korea |
Cerebral Gigantism (Sotos 증후군) 2 례 |
안희정, 김영태, 설인준, 신재훈 |
한양대학교 의과대학 소아과학교실 |
Received: 8 February 1990 • Accepted: 9 May 1990 |
|
Abstract |
Cerebral gigantism, the condition described by Sotos et al in 1964, consists of excessively rapid
growth rating from infancy followed by a normal growth rate, acromegalic features, and a non-
progressive neurological disorder manifested by clumsiness. The etiology of cerebral gigantism is not
clear. Increased growth hormone levels have not been documented and somatomedin activity was
found to be within normal range as yet reported.
We experienced two cases of cerebral gigantism in 1 10/12 and 7 year old girls with a brief review
of literatures. |
Key Words:
Cerebral Gigantism |
|