| A case of Kostmann syndrome. |
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Won Sup Shin1, Sang Woo Kim1, In Kee Paik2 |
1Department of Pediatrics, Paik Hospital in Seoul, In Je Medical Collage, Seoul, Korea
2Department of Pathology, Paik Hospital in Seoul, In Je Medical Collage, Seoul, Korea |
| Kostmann 증후군 1례 |
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신원섭1, 김상우1, 백인기2 |
1인제대학부속 백병원 소아과학교실
2인제대학부속 백병원 병리학교실 |
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Received: 13 March 1989 • Accepted: 7 July 1989 |
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| Abstract |
|
Kostmann Syndrome is an uncommon disorder, which is characterized by recurring infections,
begining soon after birth, arid by abscence of granulocyte in the peripheral blood.
The authors experienced a case of Kostmann Syndrome in a 5 months old boy who had suffered
from recurrent infection since 7 days of age. We diagnosed this case by history, physical examina-
tions, culture of bone marrow stem cell and other lab. findings. Bone marrow study in this study
disclosed morphologic details of Kostmann Syndrome.
The authors reported a case of Kostmann Syndrome with a brief review of related literatures. |
| Key Words:
Kostmann Syndrome, Agranulocytosis |
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