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A case of Marfan Syndrome.

Journal of the Korean Pediatric Society 1988;31(12):1680-1684.
Published online December 31, 1988.
A case of Marfan Syndrome.
T U Kim, S H Bae, H S Yoon, S H Kim
Department of Pediatrics, College of Medicine, Won Kwang University, I Ri, Korea
Marfan 증후군 1례
김태업, 배성호, 윤향석, 김산호
원광대학교 의과대학 소아과학교실
Received: 28 June 1988   • Accepted: 28 June 1988
Abstract
We experienced a case of Marfan syndrome in 10 year-old girl with dolichomorphism, myopia, dilatation of ascending aorta, PDA, mitral valve prolapse. Diagnosis was established by clinical characteristics with echocardiography and cardiac catheter- ization. And also, Pertinent literatures on Marfan svndrome were reviewed briefly.
Key Words: Marfan syndrome


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