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A Case of Ectopic ACTH Syndrome Caused by Wilms Tumor.

Journal of the Korean Pediatric Society 1988;31(8):1071-1078.
Published online August 31, 1988.
A Case of Ectopic ACTH Syndrome Caused by Wilms Tumor.
Dong Hun Chi, Sang Bong Han, Young Jong Woo, Tai Ju Hwang
Department of Pediatrics, School of Medicine, Chonnam National University, Kwangju, Korea
ACTH 분비 Wilms 종양에 의한 쿠싱증후군 1례
조동헌, 한상봉, 우영종, 황태주
전남대학교 의과대학 소아과학교실
Received: 5 December 1987   • Accepted: 16 March 1988
Abstract
We experienced a extremely rare case of ectopic ACTH syndrome caused by Wilms tumor in a 4 year 8 month-old female patient. We performed specific radiologic and hormonal studies. Diagnosis was confirmed by histologic and biochemical findings of tumor mass after right nephrectomy. A brief review of related literature was made.
Key Words: Ectopic ACTH Syndrome, Wilms Tumor


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