Two Cases of Congenital Asplenia. |
Man Chul Ha, Young Tak Lim, Hi Joo Chun, Hi Ju Park, Chan Yung Kim |
Department of Pediatrics, College of Medicine, Pusan National University, Pusan, Korea |
선천성 무비증 2례— 단독 무비 증 및 Ivemark 증후군 一 |
하만철, 임영탁, 전희주, 박희주, 김찬영 |
부산대학교 의과대학 소아과학교실 |
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Abstract |
Congenital absence of spleen is often associated with malpositions and malformations of other
organ system such as congenital heart disease partial situs inversus, symmetric lobulation of the liver
and the lungs. This is a rare syndrome but has been reported in increasing frequency in recent years.
The pure congenital asplenia is a very rare disease.
We experienced two cases of congenital asplenia. One is a pure congenital asplenia and the other
is an asplenia associated with congenital heart disease and partial situs inversus. The review of the
literature was made briefly. |
Key Words:
Pure congenital asplenia and asplenia syndrome associated congenital cardiac malforma-
tions and partial situs inversus.
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