A Case of Dubin-Johnson Syndrome in Childhood. |
Young Hoon Kim, Young Soo Kim, Sang Kyu Park, Jung Ki Seo, Yong Choi |
Dept, of Pediatrics, College of Medicine, Seoul National University |
Dubin-Johnson 증후군 1례 |
김영훈, 김영수, 박상규, 서정기, 최 용 |
서울대학교 의과대 학 소아과학교실 |
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Abstract |
A case of Dubin-Johnson syndrome in 10-year-old Korean male child was presented.
The presenting symptom was dark-colored urine for several years. Laboratory findings showed
increased bilirubin, especially direct-reacting bilirubin, and abnormal urinary coproporphyrin pattern (coproporphyrin I : 58%, coproporphyrin JK : 42%). Needle biopsy specimen of liver showed dark-brownish pigmentation in liver cells but was otherwise normal histologically.
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Key Words:
Dubin-Johnson syndrome. |
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