A Case of Pulmonary Arteriovenous Fistulas with Cyanosis. |
Yun Oak Rho1, Hyun Eog Yang1, Kyong Su Lee1, Kyung Sub Shin2 |
1Department of Pediatrics, Catholic Medical College, Seoul, Korea 2Department of Radiology, Catholic Medical College, Seoul, Korea |
청색증을 동반한 폐동정맥루 1례 |
노윤옥1, 양현억1, 이경수1, 신경섭2 |
1가톨릭의대 소아과학교실 2가톨릭의대 방사선과학교실 |
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Abstract |
Pulmonary arteriovenous fistula is a congenital vascular malformation in lung resulting from abnormal capillary development and thus unoxygenated, desaturated arterial blood enters into the pulmonary venous system and results in various symptoms such as exertional dyspnea, cyanosis, clubbing fingers and secondary polycythemia.
The exact etiology of pulmonary arteriovenous fistula is not well known but it may occur with or without hereditary hemorrhagic telangiectasia(Rendu-Osler-Weber syndrome). Pulmonary arteriovenous fistula often goes unrecognized early in life. Recently we experienced a case of the pulmonary arteriovenous fistulas in 15 years old
boy, which was confirmed by cardiac catheterization and pulmonary arteriography preoperatively.
Left lower lobectomy and lingular wedge resection were performed. Postoperative physiological studies showed nearly normal oxygen saturation, Hb and Rbc count. The patient had a good postoperative course and discharged.
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Key Words:
Pulmonary arteriovenous fistulas |
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