A Case of Letter-Siew Disease. |
Yoon Ho Kang1, Suck Young Lee1, Jin Sook Lee1, Kwang Ho Kim1, Soo Nam Lee2 |
1Department of Pediatrics, Inchon Christian Hospital, Inchon,Korea 2Department of Pathology, Inchon Christian Hospital, Inchon,Korea |
Letterer-Siwe 씨 병 1례 |
강윤호1, 이숙영1, 이진숙1, 김광호1, 이수남2 |
1인천기독병원 소아과 2인천기독병원 병리과 |
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Abstract |
A case of Letterer-Siwe disease in a 6 month-old Korean male manifesting maculopapular skin rash, watery diarrhea, fever and bony skull defect as classical features of the disease was presented. The diagnosis was confirmed by clinical symptoms, histopathologic and radiologic findings. The authors report a fatal case which was treated in hospital with intensive antibiotics, corticosteroid and alkylating agent.
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Key Words:
Letterer-Siwe disease |
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