| Primary Immunode Ficiency Disorders in Infancy and Childhood. |
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Hoan Jong Lee, Jung han Choi, Jeong Kee Seo, Hyo Sup Ahn, Kwang Wook Ko |
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Department of Pediatrics, College of Medicine,Seoul National University,Seoul,Korea |
| 免疫缺之疾患의 임상적 고찰 |
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李換鍾, 崔仲換, 徐起班, 安孝變, 高光昱 |
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서울醫大 小兒科學敎室 |
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| Abstract |
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The immunodeficiency disorders are a diverse group of illness which results from defectsin one or more of the four major mechanisms of immune system-antibody-mediated(B cell) immunity, cell-mediated(T cell) immunity, phagocytosis, and complements. Though immunodeficiency disorders are uncommon, the possibility should be considered in any individuals with recurrent or persistent infection. During the period between January, 1973 and October, 1984, we experienced 13 cases of primary immunodeficiency disorders-congenital agammaglobulinemia(2 cases), selective IgG deficiency(1 case), hyper-IgE syndrome(1 case), Di George syndrome(1 case), severe combined
immunodeficiency disease(2 cases), chronic granulomatous disease(2 cases), ataxia-telangie-ctasia (1 case), and chronic neutropenia(3 cases). We presented the patients briefly and reviewed the literature, with special reference to early detection and diagnosis of primary immunodeficiency disorders.
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| Key Words:
Primary immunodeficiency disorders |
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