A case of Infantile Polycystic kidney. |
Ae Sook Kim, Soon Bock Park, Young Gun Kim, Kwan Hwooy Cho, Jong Soo Kim |
Department of Pediatrics, Wonju College of Medicine,Yonsei University |
소아 양측성 다낭종신 1례 |
김애숙, 박순복, 김영건, 조관휘, 김종수 |
연세대학교 원주의과대학 소아과 |
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Abstract |
Infantile polycystic kidney is uncommon disease and rare in children and is used to refer to a group of heritable conditions that occur predominantly in childhood and is transmitted by autosomal recessive inheritance.
By developmental abnormality, multiple cysts are produced from enlargement or giantism of the collecting tubules in association with cellular hyperplasia. Kidneys are grossly enlarged and have a diffusely spongy appearence due to innumerable, radially arranged, fusiform cysts. This paper presented a case of bilateral infantile polycystic kidney in 20 day-old male baby is presented. He has respiratory distress, abdominal distension. The diagnosis of infantile polycystic kidney was made by I.V.P.
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Key Words:
Infantile polycystic kidney |
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