A Case of Acardius Twin. |
Kyung Hyo Kim1, Jung Soo Park1, Mina Lee1, Hye Kyung Lee2, Sung Sik Shin2, Je G Chi2 |
1Department of Pediatrics, Cheil Hospital 2Department of Pathology, Seoul National University Hospital, Korea |
무심 태아 1례 |
김경효1, 박정수1, 이미나1, 이혜경2, 신성식2, 지제근2 |
1제일병원 소아과 2서울대학교 의과대학 병리학교실 |
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Abstract |
A case of acardiac twins to a 30 year-old primiparous mother is presented. This case was diagnosed to have this anomaly by ultrasonography at 28 weeks and 33 weeks of gestation. The acardiac monster was delivered as the second twin without any signs of Life. It weighed 2,175 gms and was connected to the placenta by an umbilical cord having single umbilical artery. But as the placenta was missed, relationships of placental vessels between two babies were not confirmed. This acardiac baby was extremely edematous and had multiple cystic lymphangiomas in the head, neck and on upper trunk. Characteristically, there was no heart. Instead, the vascular system, consisted of parallel aorta and vena cava, would have been connected to the umbilical vessels of the first baby.Systemic organs had multiple anomalies, but extremities were relatively well developed. The first baby of the twins survived for 25 hours and died of respiratory distress. Postmortem examination revealed no other significant finding except slight cardiomegaly. This case is of particular interest in the sence of degree of differentiation of the acardiac
twin and also the association of cystic lymphangioma. A brief review is also made.
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Key Words:
Acardius twin, cystic lymphangioma |
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