| A Case of Histiocytic Medullary Reticulosis in 17 Month-old Child. |
|
Oh Kyung Lee1, Wan Seob Kim1, Myung Ho Lee1, Sung Seek Lee1, Sook Ja Park2 |
1Depart, of Pediatrics，Jeonju Presbyterian Medical Center
2Depart, of Clinical Pathology, Jeonju Presbyterian Medical Center |
| 17개월 남아에서 관찰된 조직구성 수성 망상증 1례 |
|
이오경1, 감완섭1, 이명호1, 이오경1, 박숙자2 |
1전주예수병원 소아과
2전주예수병원 임상병리과 |
|
|
|
|
| Abstract |
|
Histiocytic medullary reticulosis(HMR) is a rare, uniformly fatal, acute disease of the
reticuloen dothelial system. Major features are fever, malaise, weakness, weight loss,
lymphadenopathy, hepatosplenomegaly, jaundice and purpura. Common laboratory finding is severe pancytopenia. Cardinal pathologic feature is proliferation of atypical, neoplastic, erythrophagocytic
histiocytes. Recently we experienced a case of HMR in 17 month-old male child. The clinical findings
and hematologic features were identical to those of previously documented HMR.
In this report, we illustrate pertinent clinical and pathologic features of this disease in
early childhood and review the literature concerning this disease.
|
| Key Words:
Histiocytic medullary reticulosis. |
|
PDF Links
Download Citation
