Absence of Inferior Vena Cava. |
Sun Oak Park, Chang Yee Hong |
Department of Pediatrics, College of Medicine, Seoul National University |
下空靜脈 缺損一奇靜脈 또는 半奇靜脈과 연결을 가지는 下空靜脈의 肝下部 缺損一 |
朴善玉, 洪彩義 |
서울大學校 啓科大學 小兒科學敎室 |
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Abstract |
Out of 1617 cases of congenital heart disease, who were admitted to the Pediatric ward, Seoul National University Hospital, for cardiac catheterization during recent 5 years, 20 patients
with anomalous inferior vena cava were observed. Associated cardiac and extracardiac vascular anomalies were reviewed. Cardiac and visceral malposition were also analyzed. Results;
1) Incidence was 1.2% of total 1617 catheterized patients. 2) Male and female ratio was 8 : 12.
3) Age distribution by 5 years interval was as follows. 0〜5 years; 12 cases;5〜 10 years; 6 cases
10〜 15 years; 2 cases 4) Twelve cases of cardiac and visceral malposition were seen.
Asplenia was associated in 4 cases. Dextrocardia with situs inversus: 5 cases** Levocardia with situs inversus or ambiguus: 7 cases** 5) Associated cardiac anomalies;
Cyanotic C.H.D. 13 cases Acyanotic C.H.D.; 7 cases Single atrium 5 V.S.D. 5 Cor-biloculare 4 A.S.D. 2
Single ventricle 1 T.G.A. 1 T.O.F. 1 D.O.R.V, 1
6) In 3 cases, right mediastinal mass like shadow was observed. In lateral film, absence of LV.C. shadow below right atrium was recognized in 4 cases. 7) Arrhythmia, including 1 case of coronary sinus rhythm was noted on EKG in 7 cases 8) In 15 cases, the venous drainage was through azygos vein and in 5 cases through hemiazygos vein. 9) Persistent left superior vena cava was associated in 9 cases especially with hemiazygos continuation
(4 cases out of 5 patients with hemiazygos continuation). ****; 4 cases of asplenia
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Key Words:
Absence of I.V.C., Azygos, Hemiazygos, Malposition, Asplenia, Persistent left S.V.C.. |
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