| Two Cases of Di Guglielmo Syndrome. |
|
Seok Ku Kim1, Seong Ja Jeon1, Chul Lee1, Myung Ho Lee1, Sook Ja Park2 |
1Department of Pediatrics, Presbyterian Medical Center, Jeonju，Korea
2Department of Clinical Pathology，Presbyterian Medical Center, Jeonju，Korea |
| Di Guglielmo 증후군 2 례 |
|
김석구1, 전성자1, 이 철1, 이명호1, 박숙자2 |
1전주예수병원 소아과
2전주예수병원 임상병리과 |
|
|
|
|
| Abstract |
|
Di Guglielmo Syndrome is a relatively rare disease in childhood and refers to an acute or
chronic myeloproliferative disorder in which erythrocytes and their precursors are the cells
predominantly involved in the leukemic process. We experienced two cases of Di Guglielmo syndrome,
an llyear-old girl and a 14 year-old boy, who had the chief complaints of severe anemia, fever,
dizziness and general malasia. The Bone marrow revealed an increased pattern in the populaton of
erythroid cells including typical rubriblast, prorubriblast and bizarre multinucleated rubriblast.
One case was a stage of acute myelocytic leukemia, the other case was a stage of erythroleukemia.
|
| Key Words:
Di Guglielmo syndrome. |
|
PDF Links
Download Citation
