| A Case of Report of Letterer-Siwe Disease. |
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Nam Heon Kim1, Jung Ho Lee1, In Ho Kim1, Churl Young Chung1, Jong Eun Joo2, Ill Hyang Ko2 |
1Dept.of pediatrics, In-Je Medicial College, Seoul Korea
2Dept.of pathology, In-Je Medical College, Seoul Korea |
| Letterer-Siwe 씨 병 1 례 |
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김남헌1, 이중호1, 김인호1, 정철영1, 주종은2, 고일향2 |
1인제의대 서울백병원 소아과학교실
2인제의대 서울백병원 병리학교실 |
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| Abstract |
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We experienced a cass of Letterer-Siwe disease in 2 month old infant. The patient was presented charateristic clinical findings such as hepatosplenomegaly, petechia, anemia, gene-ralized lymphadenopathy, and lung infiltration. The diagnosis was confirmed by lymphnode biopsy and bone marrow aspiration, which was
compatible to Letterer-Siwe disease. A poor prognostic factor in Histiocytosis X is younger age (below 18 month), hepatospleno-megaly, anemia, bone marrow involvement, and hemorragic skin lesion. This patient was also poor prognostic victim as stated previously, because he was 2 month old and hepatosplenomegaly, anemia, pstechia, and bone marrow involvement.
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| Key Words:
Histiocytosis X, Letterer-Siwe disease |
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