A case of total aganglionic intestine. |
Ho Seong1, Su Dong Lee1, Don Hee Ahn1, Keun Chan Sohn1, Hea Soo Koo2, Moon Hyang Park2 |
1Department of pediatrics, National Medical Center, Korea 2Department of Pathology, National Medical Center, Korea |
先天性 全腸無神結節性 巨大結腸症 1 例 |
成 豪1, 李秀東1, 安敦姬1, 孫權贊1, 丘惠琇2, 朴文香2 |
1國立醫療院 小兒科 2國立醫療院 病理科 |
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Abstract |
A case of total aganglionic intestine in a new born infant is presented with a review of literature. Persistent vomiting, abdominal distension, failure to pass meconeum since brith were manifested. All X-rays showed multiple fluid level suggesting intestinal obstruction. In spite of colostomy with meticulous medical care, the patient expired due to cachexia. Postmortem autopsy findings were complete abscence of Auerbach's plexuses in entire intestine including esophagus, stomach, small intestine and colon. |
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