| A case of malignant atrophic papulosis (Degos' disease). |
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Sung Ku Lee1, In Seok Lim1, Chul Ha Kim1, Dong Keun Lee1, Eung Sang Choi1, Byoung Hoon Yoo1, Gae Yong Song2 |
1Department of Pediatrics, College of Medicine, Chung Ang University, Seoul, Korea
2Department of Pathology, College of Medicine, Chung Ang University, Seoul, Korea |
| 惡性妻縮性丘逐症 (Degos 病) 1例 |
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이성구1, 임인석1, 김철하1, 이동근1, 최응상1, 유병훈1, 송계용2 |
1중앙대학교 의과대학 소아과학교실
2중앙대학교 의과대학 해부병리학교실 |
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Received: 1 April 1991 • Accepted: 10 July 1991 |
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| Abstract |
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Malignant atrophic papulosis (Degos’ disease) is characterized by porcelain-white skin lesions. It
has unknown etiology and bad prognosis. Death usually occurs from multiple intestinal perforations
weeks to years after onset.
We experienced a case of Degos’ disease in a 12-year-old male patient who had porcelain white
papules on face, trunk and extremities. Histopathologic studies showed broad epidermal necrobiosis
with thrombotic arteriolar occlusion.
A brief review of related literature is also presented. |
| Key Words:
Malignant atrophic papulosis |
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