A Case of Pheochromocytoma |
Sai Youn Oh1, Byung Hae Yoon1, Keun Chan Sohn1, Keun Soo Lee1, Chui Sang Lee2, Do Hun Rha2, Kie Chung Kim3 |
1Department of Pediatrics,National Medical Center Seoul, Korea 2Department of General Surgery,National Medical Center Seoul, Korea 3Department of Radiology, National Medical Center Seoul, Korea |
小兒 Pheochromocytoma 의 1例 |
吳世鈗1, 尹炳海1, 孫槿贊1, 李謹洙1, 李喆相2, 羅燾憲2, 金基廷3 |
1國立醫療院 小兒科 2國立醫療院 一般外科 3國立醫療院 放射線科 |
|
|
Abstract |
Pheochromocytoma is a rare tumor arising from chromaffin cells of the sympatho-adrenal system which produce large amount of epinephrine and nor-epinephrine. Recently a 8year old male patient. was admitted to our Pediatric Department of National Medical Center who had suffered from sweating, polyuria polydipsia and palpitation for 3 years and hypertension was found 3 months ago, which persisted till this admission. In urine examinations, proteinuria was sustained but not glycosuria. Urinary excretion of catecholamine was markedly increased and VMA was also increased in 24 hours urine but not'so marked as catecholamine. Regitine test was positive but histamine test and BMR were not performed. Retroperitoneal pneumography showed adult-thumb tip sized soft tissue mass locating at just above the upper pole of right kidnay, which was highly suggestive of rich vascular adrenal
tumor by abdominal aortography. Right adrenalectomy was performed by surgical department. Blood pressure was stabilized after 36 hours-operation and tumor was confirmed as pheochromocytoma by histopathological study.
Two weeks after operation, he was discharged with good general condition and we report this
case with review of literatures.
|
|