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The asplenia syndrome is rare, characterized by congenital abscence of spleen, cardiovascular anomalies and other malformations or malpositions such as total or partial situs inversus, symmetrical lobulation of the liver and/or lung. Associated multiple complex cardiovascular anomalies include common atrioventricular canal, pulmonary stenosis or atresia, anomalous venous drainage and transposition of great vessels. Two-dimensional echocardiography allows the accurate non invasive... |