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Type I GSD is a metabolic disease resulted from defective glucose-6-phosphatase activities in liver,
kindey and intestine. They are characterized by growth retardation, enlargement of liver and kidney,
hypoglycemia, hyperuricemia, and hyperlipidemia.
Various methods were suggested for the management of GSD. They are night-time nasogastric
feeding of glucose solution with frequent day-time feeding, intravenous hyperalimentation, cornstarch
therapy end-to-side portacaval shunt, etc.
In this study, the effects... |
