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Case Report
A Case of Congenital Dyserythropoietic Anemia, Type II
Won Kyung Yang, Jung Wan Yoo, Hyung Goo Cho, Dong Chul Park, In Sung Lee, Won Yong Lee
Clin Exp Pediatr. 1994;37(1):99-103.   Published online January 15, 1994
Congenital dyserythropoietic anemia Type II (herditary erythroblatic multinuclearity with positive acidfied serum test;HEMPAS) is characterized by binuclearity, multinuclearity, pluripolar mitoses, karyorrhexis of normoblasts, and the presence of abnormla antigens on the red cells. We experienced a case of HEMPAS in a 2 month old girl patient who had an intermittent fever, abdominal distention with palpable liver & spleen, and generalized jaundice. The...
A Case of Congenital Dyserythropoietic Anemia
Il Tae Whang, Young Sook Ko, Kyeung Hee Kim, Gyeung In Lee, Han Ik Cho
Clin Exp Pediatr. 1992;35(4):539-544.   Published online April 15, 1992
Congenital dyserythropoietic anemia(CDA) is a rare disease characterized by ineffective erythropoiesis, specific cytopathology of the nucleated red cells in the bone marrow and secondary hemochromatosis. CDA is classified into 4 types on the basis of results of electron microscopic and serologic studies. We experienced a case of congenital dyserythropoietic anemia in a 5/12 year-old boy. Diagnosis was established by macrocytosis, anisopoikilocytosis in PB...