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Original Article
A Case of Werdnig-Hoffmann Disease.
Ok Ji Hwang, Kon Hee Lee, Ha Joo Choi, Woo Kap Chung
Clin Exp Pediatr. 1989;32(2):289-296.   Published online February 28, 1989
Acute Werdnig-Hoffmann disease is heredofamilial degeneration of anterior horn cells in the spinal cord and of motor nuclei in the brain stem, which is clinically characterized by fasciculations of the tongue, paradoxical respiration, bell shaped thorax, frog-leg posture and intact mentality. We experienced an 8 month old female infant with acute Werdnig-Hoffmann disease. We report the case with brief review of some related literatures.
A Case of Human Tail.
Kon Hee Lee, Ok Ji Hwang, Ha Joo Choi, Woo Kap Chung
Clin Exp Pediatr. 1989;32(2):285-288.   Published online February 28, 1989
The human tail is thought to be a rare congenital anomaly which resulted from persistence of the vestigial tail of the 14 -16 mm. human embryo. A child with a tail causes for the parents and, in some cases, a feeling of stigma and shame. We experienced a case of human tail who was an 1-day old male. Examination of the baby revealed a...
Histiocytic Medullart Reticuloisis in Children.
Duck Kyu Kim, Jung Hyun Park, Ok Ji Hwang, Ja Ye Kim, Woo Kap Chung, Kye Sook Lee
Clin Exp Pediatr. 1988;31(9):1217-1224.   Published online September 30, 1988
Histiocytic medullary reticulosis (HMR) is a clinicopathologic syndrome characterized by its acute onset and relentless progression to death within a few months. Major clinical features are fever, wasting, generalized lymphadenopathy and hepatosplenomegaly. In the terminal stages, Jaundice, purpura, anemia and leukopenia are common. Cardinal pathologic features are diffuse proliferation of atypical, neoplastic, erythrophagocytic histiocytes and their precursors throughout the reticuloen- dothelial system. Here, we present 2...