| Seven Cases of Immotile Cilia Syndrome |
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Sun Young Lee1, Myung Ik Lee1, Don Hee Ahn1, Keun Chan Sohn1, Je Geun Chi2 |
1Department of Pediatrics, National Medical Center, Seoul, Korea
2Department of Pathology, Seoul National University, College of Medicine, Seoul, Korea |
| Immotile Cilia Syndrome 7ë¡€ |
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| Abstract |
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Immotile cilia syndrome is a disease caused by congenital abnormality of the cilia and symptom complex composed by chronic rhinitis, sinusitis, otitis, male infertility etc.
We have experienced 7 cases of immotile cilia syndrome diagnosed by electron microscopic finding of nasal or bronchial mucosal biopsies since 1984. Six cases were girls and type Id was most common (4 cases) on electron microscopic classification. And most of the patients showed gradual improvement with supportive therapy in several years.
We reported 7 cases with review of related literature. |
| Key Words:
Immotile cilia syndrome |
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